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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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NPR1
natriuretic peptide receptor 1
Chromosome 1 · 1q21.3
NCBI Gene: 4881Ensembl: ENSG00000169418.11HGNC: HGNC:7943UniProt: A0A140VJE6
101PubMed Papers
20Diseases
3Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Receptor
CLINICAL
FDA Approved Target
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
receptor guanylyl cyclase signaling pathwaypeptide hormone bindingnatriuretic peptide receptor activityregulation of blood pressurecongestive heart failurecardiovascular diseasehypertensionheart failure
✦AI Summary

NPR1 (natriuretic peptide receptor 1) is a membrane-bound guanylate cyclase receptor that functions as the primary effector for natriuretic peptides ANP and BNP 1. Upon ligand binding, NPR1 stimulates cGMP production, activating protein kinase cGMP-dependent 1 (PRKG1), which subsequently activates PRKAA1 to regulate vascular tone and blood pressure homeostasis 2. NPR1 plays an essential role in endothelial cell senescence regulation and vascular aging [UniProt Function]. In heart failure, NPR1 activation promotes vasodilation, diuresis, and natriuresis, lowering venous pressures and congestion 3. Genetic variants in NPR1 are associated with blood pressure changes and heart failure risk in large population studies 3. Beyond cardiovascular function, NPR1 promotes gastric cancer metastasis by activating lipid droplet lipolysis through PRKG1-mediated phosphorylation of hormone-sensitive lipase, enhancing mitochondrial oxidative phosphorylation and fueling cancer cell energy demands 2. Elevated NPR1 correlates with increased lymph node metastasis and shorter survival in gastric cancer patients 2. NPR1 agonists represent promising therapeutic targets for resistant hypertension and heart failure, with monoclonal agonist antibodies like REGN5381 demonstrating selective venous pressure reduction in clinical trials 13.

Sources cited
1
NPR1 agonists are therapeutic targets for hypertension and resistant hypertension
PMID: 38849267
2
NPR1 activation regulates vascular tone, diuresis, and natriuresis; NPR1 variants associated with blood pressure and heart failure risk
PMID: 39261724
3
NPR1 promotes gastric cancer metastasis through PRKG1-mediated lipid droplet lipolysis and OXPHOS enhancement; elevated NPR1 correlates with lymph node metastasis and reduced survival
PMID: 40539884
⚠Limited data available — This gene has 3 indexed publications. Summary and analysis may be incomplete.
Disease Associationsⓘ20
congestive heart failureOpen Targets
0.58Moderate
cardiovascular diseaseOpen Targets
0.44Moderate
hypertensionOpen Targets
0.41Moderate
heart failureOpen Targets
0.39Weak
cardiomyopathyOpen Targets
0.33Weak
Increased blood pressureOpen Targets
0.29Weak
kidney diseaseOpen Targets
0.26Weak
DyspneaOpen Targets
0.26Weak
neurodegenerative diseaseOpen Targets
0.23Weak
essential hypertensionOpen Targets
0.23Weak
early onset hypertensionOpen Targets
0.13Weak
asthmaOpen Targets
0.10Suggestive
gastric cancerOpen Targets
0.10Suggestive
dilated cardiomyopathyOpen Targets
0.10Suggestive
infectionOpen Targets
0.10Suggestive
neoplasmOpen Targets
0.09Suggestive
posterior cortical atrophyOpen Targets
0.08Suggestive
hyperaldosteronism, familial, type IVOpen Targets
0.08Suggestive
metabolic syndromeOpen Targets
0.08Suggestive
dilated cardiomyopathy 1EEOpen Targets
0.08Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Drug Targets3
CARPERITIDEApproved
Atrial natriuretic peptide receptor agonist
congestive heart failure
NESIRITIDEApproved
Atrial natriuretic peptide receptor A agonist
cardiovascular disease
PL-3994Phase II
Atrial natriuretic peptide receptor A agonist
asthma
Related Genes
PLXNA1Protein interaction100%PDE6GProtein interaction100%PDE6BProtein interaction98%PDE1CProtein interaction96%NPPCProtein interaction95%GNASProtein interaction95%
Tissue Expression6 tissues
Ovary
100%
Lung
84%
Heart
44%
Liver
14%
Brain
2%
Bone Marrow
0%
Gene Interaction Network
Click a node to explore
NPR1PLXNA1PDE6GPDE6BPDE1CNPPCGNAS
PROTEIN STRUCTURE
Preparing viewer…
PDB9BCL · 2.90 Å · EM
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.67LoF Tolerant
pLIⓘ
0.00Tolerant
Observed/Expected LoF0.54 [0.43–0.67]
RankingsWhere NPR1 stands among ~20K protein-coding genes
  • #4,730of 20,598
    Most Researched101 · top quartile
  • #599of 1,025
    FDA-Approved Drug Targets2
  • #4,945of 17,882
    Most Constrained (LOEUF)0.67
Genes detectedNPR1
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
New therapeutic targets in hypertension.
PMID: 38849267
Med Clin (Barc) · 2024
1.00
2
Agonist antibody to guanylate cyclase receptor NPR1 regulates vascular tone.
PMID: 39261724
Nature · 2024
0.90
3
Structural basis of NPR1 in activating plant immunity.
PMID: 35545668
Nature · 2022
0.80
4
NPR1 promotes cisplatin resistance by inhibiting PARL-mediated mitophagy-dependent ferroptosis in gastric cancer.
PMID: 39476297
Cell Biol Toxicol · 2024
0.70
5
NPR1 Promotes Lipid Droplet Lipolysis to Enhance Mitochondrial Oxidative Phosphorylation and Fuel Gastric Cancer Metastasis.
PMID: 40539884
Adv Sci (Weinh) · 2025
0.60