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GeneE
7 sources retrieved · Most recent: April 2026 · Index updated 15 days ago
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ZC3H10
zinc finger CCCH-type containing 10
Chromosome 12 · 12q13.2
NCBI Gene: 84872Ensembl: ENSG00000135482.8HGNC: HGNC:25893UniProt: Q96K80
29PubMed Papers
16Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
miRNA bindingRNA bindingprotein bindingnucleusneurodegenerative diseaseAbnormality of the skeletal systemgliomasquamous cell carcinoma
✦AI Summary

ZC3H10 is a CCCH-type zinc finger protein with dual functions in gene regulation and cellular metabolism. As a post-transcriptional regulator, ZC3H10 binds to specific RNA sequences (5'-GCAGCGC-3') on pri-miR143 through its zinc finger domains to negatively regulate miRNA processing 1. Beyond miRNA regulation, ZC3H10 functions as a transcription factor activating the UCP1 promoter in brown adipose tissue thermogenesis. Upon sympathetic stimulation, p38 MAPK phosphorylates ZC3H10 at S126, enhancing its binding to the distal UCP1 promoter region and promoting thermogenic gene expression 2. ZC3H10 also acts as a mitochondrial regulator; its upregulation during myoblast differentiation enhances mitochondrial function and electron transport chain expression, while depletion impairs mitochondrial physiology and myoblast differentiation 3. A human loss-of-function mutation (Tyr105Cys) associates with metabolic dysfunction including increased body mass index and reduced oxygen consumption 3. Clinically, ZC3H10 appears tumor-suppressive, inhibiting anchorage-independent growth in breast cancer cells 4, and influences glioma chemotherapy sensitivity to temozolomide 5. These findings suggest ZC3H10 as a therapeutic target for obesity and cancer management.

Sources cited
1
ZC3H10 is an RNA-binding protein that regulates miRNA biogenesis
PMID: 28431233
2
ZC3H10 functions as a transcription factor activating UCP1 in brown adipose tissue thermogenesis through p38 MAPK phosphorylation
PMID: 31775033
3
ZC3H10 regulates mitochondrial function and a human Tyr105Cys mutation associates with metabolic dysfunction
PMID: 29507079
4
ZC3H10 inhibits anchorage-independent growth suggesting tumor suppressor function
PMID: 18814840
5
ZC3H10 influences glioma cell sensitivity to temozolomide chemotherapy
PMID: 31953347
6
ZC3H10 is among key transcriptional regulators of the brown adipose thermogenic gene program
PMID: 32219439
Disease Associationsⓘ16
neurodegenerative diseaseOpen Targets
0.37Weak
Abnormality of the skeletal systemOpen Targets
0.13Weak
gliomaOpen Targets
0.03Suggestive
squamous cell carcinomaOpen Targets
0.02Suggestive
obesityOpen Targets
0.02Suggestive
basal cell carcinomaOpen Targets
0.02Suggestive
intelligenceOpen Targets
0.02Suggestive
rheumatoid arthritisOpen Targets
0.02Suggestive
type 1 diabetes mellitusOpen Targets
0.02Suggestive
neoplasmOpen Targets
0.01Suggestive
breast cancerOpen Targets
0.00Suggestive
Global developmental delayOpen Targets
0.00Suggestive
colorectal carcinomaOpen Targets
0.00Suggestive
esophageal cancerOpen Targets
0.00Suggestive
ovarian serous cystadenocarcinomaOpen Targets
0.00Suggestive
uterine corpus endometrial carcinomaOpen Targets
0.00Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
RBM12BShared pathway50%AHNAK2Shared pathway50%ESRP2Shared pathway50%AHNAKShared pathway50%CLK4Shared pathway50%MBNL3Shared pathway50%
Tissue Expression6 tissues
Ovary
100%
Heart
80%
Lung
72%
Liver
71%
Brain
71%
Bone Marrow
39%
Gene Interaction Network
Click a node to explore
ZC3H10RBM12BAHNAK2ESRP2AHNAKCLK4MBNL3
PROTEIN STRUCTURE
Preparing viewer…
AlphaFoldAI-predicted · UniProt Q96K80
View on AlphaFold ↗
Constraintⓘ
LOEUFⓘ
0.78LoF Tolerant
pLIⓘ
0.05Tolerant
Observed/Expected LoF0.48 [0.31–0.78]
RankingsWhere ZC3H10 stands among ~20K protein-coding genes
  • #12,277of 20,598
    Most Researched29
  • #6,369of 17,882
    Most Constrained (LOEUF)0.78
Genes detectedZC3H10
Sources retrieved7 papers
Response time—
📄 Sources
7▼
1
Pan-primate studies of age and sex.
PMID: 37493860
Geroscience · 2023
1.00
2
Zc3h10 Acts as a Transcription Factor and Is Phosphorylated to Activate the Thermogenic Program.
PMID: 31775033
Cell Rep · 2019
0.86
3
Epigenetic dynamics of the thermogenic gene program of adipocytes.
PMID: 32219439
Biochem J · 2020
0.71
4
Zc3h10 is a novel mitochondrial regulator.
PMID: 29507079
EMBO Rep · 2018
0.57
5
Gene trapping identifies a putative tumor suppressor and a new inducer of cell migration.
PMID: 18814840
Biochem Biophys Res Commun · 2008
0.43