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28 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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TSG101
tumor susceptibility 101
Chromosome 11 · 11p15.1
NCBI Gene: 7251Ensembl: ENSG00000074319.14HGNC: HGNC:15971UniProt: Q99816
380PubMed Papers
20Diseases
1Drugs
0Pathogenic Variants
FUNCTIONAL ROLE
Hub GeneTransporter
RESEARCH IMPACT
Highly Studied
CLINICAL
Early Pipeline
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
positive regulation of exosomal secretionregulation of extracellular exosome assemblypositive regulation of viral budding via host ESCRT complexplasma membraneHIV infectionviral diseasedengue diseaseneurodegenerative disease
✦AI Summary

TSG101 is a multidomain protein and core component of the ESCRT-I complex that regulates vesicular trafficking and cellular homeostasis 1. Its primary function involves binding ubiquitinated cargo proteins and sorting them into multivesicular bodies for endosomal degradation 2. TSG101 is essential for cytokinesis completion and mediates ESCRT-0 to ESCRT-I complex transitions 1. The protein also regulates exosomal release of cargo molecules including CD63 and syndecan, with evidence supporting roles in extracellular microvesicle biogenesis 3. Beyond endosomal sorting, TSG101 plays critical roles in innate immunity by facilitating STING degradation through ESCRT-dependent microautophagy, preventing hyperactivation of interferon responses 4. TSG101 is also recruited to endolysosomal damage sites where it participates in membrane repair mechanisms 5. Clinically significant is TSG101's hijacking by enveloped viruses: the P(T/S)AP-binding pocket in TSG101's N-terminal domain recruits viral late-budding motifs, enabling HIV-1 and coronavirus budding and replication 67. TSG101 depletion impairs viral particle release, making it an attractive anti-viral therapeutic target 8. Additionally, TSG101 functions as a negative growth regulator implicated in tumorigenesis 1, suggesting potential relevance in cancer biology.

Sources cited
1
TSG101 is a multidomain ESCRT-I component involved in endosomal sorting, cytokinesis, ubiquitination, transcriptional regulation, cell cycle, and tumorigenesis
PMID: 23276921
2
TSG101 recognizes ubiquitinated cargo and is essential for HIV-1 budding and vacuolar protein sorting
PMID: 20088757
3
TSG101 is a component of exosomes (marked by CD63 and TSG101 positivity) involved in exosomal cargo release
PMID: 29556344
4
TSG101 is essential for STING degradation through ESCRT-dependent microautophagy and prevents sustained interferon responses
PMID: 36918692
5
ESCRT machinery including TSG101 plays a role in repair of acutely injured endolysosomes
PMID: 29622626
6
TSG101's N-terminal P(T/S)AP-binding pocket recruits viral late-budding motifs from HIV-1 Gag protein
PMID: 34203832
7
TSG101 is essential for alphacoronavirus entry and replication through roles in endocytosis and replication site organization
PMID: 38489378
8
TSG101 facilitates HIV-1 viral budding and represents a target for antibody-based anti-HIV therapies
PMID: 29199609
Disease Associationsⓘ20
HIV infectionOpen Targets
0.53Moderate
viral diseaseOpen Targets
0.47Moderate
dengue diseaseOpen Targets
0.37Weak
neurodegenerative diseaseOpen Targets
0.34Weak
AlkalosisOpen Targets
0.16Weak
Peyronie diseaseOpen Targets
0.15Weak
neoplasmOpen Targets
0.10Suggestive
hepatocellular carcinomaOpen Targets
0.10Suggestive
breast cancerOpen Targets
0.09Suggestive
renal cell carcinomaOpen Targets
0.07Suggestive
infectionOpen Targets
0.07Suggestive
cancerOpen Targets
0.06Suggestive
nasopharyngeal carcinomaOpen Targets
0.06Suggestive
influenzaOpen Targets
0.05Suggestive
lung cancerOpen Targets
0.04Suggestive
cervical cancerOpen Targets
0.03Suggestive
gliomaOpen Targets
0.03Suggestive
glomerulonephritisOpen Targets
0.03Suggestive
ovarian cancerOpen Targets
0.03Suggestive
ischemiaOpen Targets
0.03Suggestive
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Drug Targets1
FGI-101-1A6Phase I
Tumor susceptibility gene 101 protein inhibitor
influenza
Related Genes
CEP55Protein interaction100%PDCD6IPProtein interaction100%CHMP3Protein interaction100%UBCProtein interaction100%ARRDC1Protein interaction100%CHMP2AProtein interaction100%
Tissue Expression6 tissues
Heart
100%
Brain
83%
Bone Marrow
73%
Lung
66%
Liver
58%
Ovary
57%
Gene Interaction Network
Click a node to explore
TSG101CEP55PDCD6IPCHMP3UBCARRDC1CHMP2A
PROTEIN STRUCTURE
Preparing viewer…
PDB3OBQ · 1.40 Å · X-ray
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.65LoF Tolerant
pLIⓘ
0.12Tolerant
Observed/Expected LoF0.43 [0.30–0.65]
RankingsWhere TSG101 stands among ~20K protein-coding genes
  • #795of 20,598
    Most Researched380 · top 5%
  • #4,720of 17,882
    Most Constrained (LOEUF)0.65
Genes detectedTSG101
Sources retrieved28 papers
Response time—
📄 Sources
28▼
1
Triggered recruitment of ESCRT machinery promotes endolysosomal repair.
PMID: 29622626
Science · 2018
1.00
2
Exosomal DMBT1 from human urine-derived stem cells facilitates diabetic wound repair by promoting angiogenesis.
PMID: 29556344
Theranostics · 2018
0.90
3
ESCRT-I and PTPN23 mediate microautophagy of ubiquitylated tau aggregates.
PMID: 40197510
J Cell Biol · 2025
0.88
4
STING signalling is terminated through ESCRT-dependent microautophagy of vesicles originating from recycling endosomes.
PMID: 36918692
Nat Cell Biol · 2023
0.80
5
Peptide inhibitors of HIV-1 egress.
PMID: 19099395
ACS Chem Biol · 2008
0.80