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10 sources retrieved · Most recent: April 2026 · Index updated 14 days ago
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CPEB3
cytoplasmic polyadenylation element binding protein 3
Chromosome 10 · 10q23.32
NCBI Gene: 22849Ensembl: ENSG00000107864.16HGNC: HGNC:21746UniProt: B3KXC1
42PubMed Papers
20Diseases
0Drugs
0Pathogenic Variants
DATA QUALITY
✓ Experimental GO Evidence✓ Swiss-Prot Reviewed
negative regulation of translationtranslation factor activity, RNA bindingCCR4-NOT complexpositive regulation of nuclear-transcribed mRNA poly(A) tail shorteningtype 2 diabetes mellitusdiabetes mellitusschizophreniaattention deficit hyperactivity disorder
✦AI Summary

CPEB3 (cytoplasmic polyadenylation element binding protein 3) is a sequence-specific RNA-binding protein that serves as a critical regulator of synaptic plasticity and memory formation. CPEB3 functions as a translational switch, acting as a repressor in the basal state but becoming a translational activator following neuronal stimulation 1. The protein regulates translation of key synaptic proteins including AMPA receptor subunits (GRIA1, GRIA2), NMDA receptor subunits (GRIN1, GRIN2A, GRIN2B), and scaffolding proteins like PSD95, which are essential for synaptic plasticity and long-term memory consolidation 1. CPEB3 contains a self-cleaving ribozyme in its second intron that affects episodic memory performance 2. Structurally, the protein features an amyloid-forming segment (L103-F151) that is crucial for proper cellular localization and function, as deletion of this region results in abnormal cellular puncta formation and loss of translational control 3. CPEB3 demonstrates neuroprotective properties, with its deletion protecting against excitotoxicity and neuroinflammation in experimental models 4. In epilepsy, CPEB3 functions as a negative regulator of seizure susceptibility by inhibiting STAT3 transcriptional activity and subsequently reducing NMDAR expression 5. The protein also plays important roles in cancer suppression, particularly in hepatocellular carcinoma, by suppressing translation of oncogenic targets like MTDH 6.

Sources cited
1
CPEB3 functions as translational switch and regulates synaptic proteins for memory formation
PMID: 32619199
2
CPEB3 contains a self-cleaving ribozyme affecting episodic memory
PMID: 21734469
3
CPEB3 contains amyloid-forming segment essential for proper cellular function
PMID: 40480223
4
CPEB3 deletion provides neuroprotection against excitotoxicity and neuroinflammation
PMID: 38000031
5
CPEB3 negatively regulates seizure susceptibility via STAT3-NMDAR pathway
PMID: 39994587
6
CPEB3 suppresses hepatocellular carcinoma progression through MTDH regulation
PMID: 32968053
Disease Associationsⓘ20
type 2 diabetes mellitusOpen Targets
0.42Moderate
diabetes mellitusOpen Targets
0.30Weak
schizophreniaOpen Targets
0.29Weak
attention deficit hyperactivity disorderOpen Targets
0.28Weak
glaucomaOpen Targets
0.23Weak
Visual impairmentOpen Targets
0.23Weak
type 1 diabetes mellitusOpen Targets
0.22Weak
cataractOpen Targets
0.22Weak
breast cancerOpen Targets
0.21Weak
hepatocellular carcinomaOpen Targets
0.21Weak
melanomaOpen Targets
0.20Weak
lung adenocarcinomaOpen Targets
0.20Weak
clear cell renal carcinomaOpen Targets
0.19Weak
acute myeloid leukemiaOpen Targets
0.19Weak
gastric adenocarcinomaOpen Targets
0.19Weak
ovarian serous adenocarcinomaOpen Targets
0.19Weak
urinary bladder carcinomaOpen Targets
0.19Weak
colorectal adenocarcinomaOpen Targets
0.18Weak
Hepatobiliary NeoplasmOpen Targets
0.18Weak
rectal adenocarcinomaOpen Targets
0.18Weak
Pathogenic Variants
No pathogenic variants reported on ClinVar for this gene.
View on ClinVar ↗
Related Genes
CNOT10Protein interaction100%CNOT1Protein interaction100%CNOT11Protein interaction100%CNOT6Protein interaction100%CNOT7Protein interaction100%CNOT6LProtein interaction100%
Tissue Expression6 tissues
Brain
100%
Liver
77%
Heart
66%
Bone Marrow
37%
Ovary
25%
Lung
14%
Gene Interaction Network
Click a node to explore
CPEB3CNOT10CNOT1CNOT11CNOT6CNOT7CNOT6L
PROTEIN STRUCTURE
Preparing viewer…
PDB7N2E · 1.00 Å · EM
View on RCSB ↗
Constraintⓘ
LOEUFⓘ
0.58Moderately Constrained
pLIⓘ
0.60Intermediate
Observed/Expected LoF0.39 [0.26–0.58]
RankingsWhere CPEB3 stands among ~20K protein-coding genes
  • #9,856of 20,598
    Most Researched42
  • #3,936of 17,882
    Most Constrained (LOEUF)0.58 · top quartile
Genes detectedCPEB3
Sources retrieved10 papers
Response time—
📄 Sources
10▼
1
MicroRNA-92a-CPEB3 axis protects neurons against inflammatory neurodegeneration.
PMID: 38000031
Sci Adv · 2023
1.00
2
Role of CPEB3 protein in learning and memory: new insights from synaptic plasticity.
PMID: 32619199
Aging (Albany NY) · 2020
0.90
3
CPEB3 can regulate seizure susceptibility by inhibiting the transcriptional activity of STAT3 on NMDARs expression.
PMID: 39994587
Mol Med · 2025
0.80
4
HDV-like self-cleaving ribozymes.
PMID: 21734469
RNA Biol · 2011
0.70
5
Solution structure and metal ion binding sites of the human CPEB3 ribozyme's P4 domain.
PMID: 24652468
J Biol Inorg Chem · 2014
0.60